{"id":3408,"date":"2016-06-23T10:05:38","date_gmt":"2016-06-23T10:05:38","guid":{"rendered":"http:\/\/dweb.pfsgrupo.com\/hospitalcardona\/blog\/2019\/07\/26\/que-es-la-ela\/"},"modified":"2016-06-23T10:05:38","modified_gmt":"2016-06-23T10:05:38","slug":"que-es-la-ela","status":"publish","type":"post","link":"https:\/\/riberasalud.com\/juan-cardona\/2016\/06\/23\/que-es-la-ela\/","title":{"rendered":"\u00bfQu\u00e9 es la ELA?","gt_translate_keys":[{"key":"rendered","format":"text"}]},"content":{"rendered":"<p>Publicado por Hospital Juan Cardona el 23 de junio de 2016 13:00:00 CEST<\/p>\n<div class=\"body-container-wrapper\">\n<div class=\"body-container container-fluid\">\n<div class=\"row-fluid-wrapper row-depth-1 row-number-3 \">\n<div class=\"row-fluid \">\n<div class=\"span12 widget-span widget-type-cell contenido-post-2columnas-blog\" data-widget-type=\"cell\" data-x=\"0\" data-w=\"12\">\n<div class=\"row-fluid-wrapper row-depth-1 row-number-4 \">\n<div class=\"row-fluid \">\n<div class=\"span12 widget-span widget-type-cell page-center caja-contenido-blog\" data-widget-type=\"cell\" data-x=\"0\" data-w=\"12\">\n<div class=\"row-fluid-wrapper row-depth-1 row-number-5 \">\n<div class=\"row-fluid \">\n<div class=\"span8 widget-span widget-type-cell \" data-widget-type=\"cell\" data-x=\"0\" data-w=\"8\">\n<div class=\"row-fluid-wrapper row-depth-1 row-number-6 \">\n<div class=\"row-fluid \">\n<div class=\"span12 widget-span widget-type-blog_content \" data-widget-type=\"blog_content\" data-x=\"0\" data-w=\"12\">\n<div class=\"blog-section\">\n<div class=\"blog-post-wrapper cell-wrapper\">\n<div class=\"section post-header clearfix\">\n<p><!-- AUTOR --><\/p>\n<\/div>\n<div class=\"section post-body\">\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-3473\" src=\"https:\/\/riberasalud.com\/juan-cardona\/wp-content\/uploads\/2019\/07\/ela.jpg\" alt=\"\" width=\"1363\" height=\"696\" \/><\/p>\n<p>La <span style=\"color: #ff255a;\">Esclerosis Lateral Amiotr\u00f3fica (ELA)<\/span> es una enfermedad neuromuscular que cursa con una degeneraci\u00f3n selectiva de las motoneuronas , las encargadas de innervar los m\u00fasculos implicados en el movimiento voluntario.<br \/>\n<!--more--><br \/>\n\u00bfPorqu\u00e9 este nombre, qu\u00e9 significa? el t\u00e9rmino \u201cesclerosis lateral\u201d hace referencia a la afectaci\u00f3n de las fibras nerviosas de la parte lateral de la m\u00e9dula espinal as\u00ed como a la gliosis (proliferaci\u00f3n de astr\u00f3citos, un tipo de c\u00e9lula glial) que se da y el de \u201camiotr\u00f3fica\u201d a la atrofia muscular que se produce cuando los m\u00fasculos dejan de recibir se\u00f1ales nerviosas.<\/p>\n<p>La consecuencia es una debilidad muscular progresiva que <span style=\"color: #ff255a;\">avanza hacia la par\u00e1lisis total del enfermo vi\u00e9ndose afectadas tambi\u00e9n la capacidad de hablar, masticar, tragar y respirar<\/span>. Por otro lado funciones como la sensibilidad y la inteligencia no se ven afectados y tampoco los movimientos oculares ya que se trata motoneuronas que poseen m\u00e1s resistencia.<\/p>\n<p>La enfermedad <span style=\"color: #ff255a;\">se diagnostica mayoritariamente entre los 40 y 70 a\u00f1os de edad, aunque puede afectar a un rango mucho m\u00e1s amplio de edades, y es m\u00e1s frecuente en varones<\/span>. Cada a\u00f1o se diagnostican 2 casos de ELA por cada 100.000 habitantes que en Espa\u00f1a vendr\u00edan a ser unos 900 casos nuevos cada a\u00f1o. La esperanza de vida despu\u00e9s del diagn\u00f3stico es de 5 a\u00f1os para el 80% de los pacientes y la evoluci\u00f3n de la enfermedad puede variar mucho de un afectado respecto a otro.<\/p>\n<p>En la mayor\u00eda de los casos (90-95%) la ELA se presenta de forma espor\u00e1dica y sin origen conocido pero existe tambi\u00e9n un tipo de ELA familiar de car\u00e1cter hereditario. En este caso la causa m\u00e1s descrita reside en una <span style=\"color: #ff255a;\">mutaci\u00f3n que afecta a la enzima antioxidante Superoxido Dismutasa 1 (SOD1)<\/span>. Tambi\u00e9n se han encontrado casos de ELA espor\u00e1dica con esta mutaci\u00f3n. Por esto y porqu\u00e9 reproducen muchos mecanismos de la enfermedad, los ratones con mutaci\u00f3n en la SOD 1 son el modelo m\u00e1s utilizado en investigaci\u00f3n. A pesar de esto, actualmente, se sabe que hay muchos genes candidatos a estar implicados en la enfermedad y tambi\u00e9n se est\u00e1n estudiando otros mecanismos patog\u00e9nicos como la excitotoxicidad ( producida exceso del neurotransmisor excitador glutamato), estr\u00e9s oxidativo (radicales oxidantes, disfunci\u00f3n mitocondrial), fallo en el transporte axopl\u00e1smico o autoimunidad (anticuerpos contra canales de calcio) y neuroinflamaci\u00f3n.<\/p>\n<p>Ya hace m\u00e1s de 140 a\u00f1os que la enfermedad fue descrita por el neur\u00f3logo franc\u00e9s Jean-Martin Charcot pero hoy en d\u00eda todav\u00eda se carece de una terapia efectiva para su tratamiento. El \u00fanico f\u00e1rmaco autorizado actualmente para la ELA es el riluzole (Rilutek ) del que se han demostrado unos escasos e insuficientes beneficios que alargan la vida del paciente de 2 a 3 meses.<\/p>\n<p>Por esto es tan importante fomentar la investigaci\u00f3n y los ensayos cl\u00ednicos en pacientes con f\u00e1rmacos en los que se haya demostrado la eficacia y seguridad y que podr\u00edan ser beneficiosos, con factores neurotr\u00f3ficos (sustancias que favorecen la supervivencia neuronal as\u00ed como la regeneraci\u00f3n axonal) o con c\u00e9lulas madre.<\/p>\n<p>En el Hospital Juan Cardona contamos con un <a href=\"https:\/\/riberasalud.com\/juan-cardona\/servicio-de-neurologia-en-el-hospital-juan-cardona-0\/\" target=\"_blank\" rel=\"noopener noreferrer\">servicio de Neurolog\u00eda<\/a>\u00a0que pone a su disposici\u00f3n las m\u00e1s avanzadas <a href=\"https:\/\/riberasalud.com\/juan-cardona\/pruebas-diagnosticas\/\" target=\"_blank\" rel=\"noopener noreferrer\">t\u00e9cinicas diagn\u00f3sticas.<\/a><\/p>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n","protected":false,"gt_translate_keys":[{"key":"rendered","format":"html"}]},"excerpt":{"rendered":"<p>En el post de hoy queremos divulgar informaci\u00f3n sobre qu\u00e9 es la ELA, enfermedad neuromuscular con m\u00e1s incidencia de la que pensamos.<\/p>\n","protected":false,"gt_translate_keys":[{"key":"rendered","format":"html"}]},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[4],"tags":[],"class_list":["post-3408","post","type-post","status-publish","format-standard","hentry","category-noticias-del-hospital-juan-cardona"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.6 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>\u00bfQu\u00e9 es la ELA? 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