{"id":3401,"date":"2016-04-21T10:05:37","date_gmt":"2016-04-21T10:05:37","guid":{"rendered":"http:\/\/dweb.pfsgrupo.com\/hospitalcardona\/blog\/2019\/07\/26\/fibrosis-quistica\/"},"modified":"2016-04-21T10:05:37","modified_gmt":"2016-04-21T10:05:37","slug":"fibrosis-quistica","status":"publish","type":"post","link":"https:\/\/riberasalud.com\/juan-cardona\/2016\/04\/21\/fibrosis-quistica\/","title":{"rendered":"Fibrosis qu\u00edstica","gt_translate_keys":[{"key":"rendered","format":"text"}]},"content":{"rendered":"<p>Publicado por Hospital Juan Cardona el 21 de abril de 2016 11:19:00 CEST<\/p>\n<div class=\"body-container-wrapper\">\n<div class=\"body-container container-fluid\">\n<div class=\"row-fluid-wrapper row-depth-1 row-number-3 \">\n<div class=\"row-fluid \">\n<div class=\"span12 widget-span widget-type-cell contenido-post-2columnas-blog\" data-widget-type=\"cell\" data-x=\"0\" data-w=\"12\">\n<div class=\"row-fluid-wrapper row-depth-1 row-number-4 \">\n<div class=\"row-fluid \">\n<div class=\"span12 widget-span widget-type-cell page-center caja-contenido-blog\" data-widget-type=\"cell\" data-x=\"0\" data-w=\"12\">\n<div class=\"row-fluid-wrapper row-depth-1 row-number-5 \">\n<div class=\"row-fluid \">\n<div class=\"span8 widget-span widget-type-cell \" data-widget-type=\"cell\" data-x=\"0\" data-w=\"8\">\n<div class=\"row-fluid-wrapper row-depth-1 row-number-6 \">\n<div class=\"row-fluid \">\n<div class=\"span12 widget-span widget-type-blog_content \" data-widget-type=\"blog_content\" data-x=\"0\" data-w=\"12\">\n<div class=\"blog-section\">\n<div class=\"blog-post-wrapper cell-wrapper\">\n<div class=\"section post-header clearfix\">\n<p><!-- AUTOR --><\/p>\n<\/div>\n<div class=\"section post-body\">\n<p><img loading=\"lazy\" decoding=\"async\" class=\"size-full wp-image-3741 aligncenter\" src=\"https:\/\/riberasalud.com\/juan-cardona\/wp-content\/uploads\/2019\/07\/fibrosis_quistica.jpg\" alt=\"\" width=\"898\" height=\"394\" \/><\/p>\n<p>El pr\u00f3ximo d\u00eda 25 de abril se conmemora el <span style=\"color: #ff255a;\">D\u00eda Mundial de la Fibrosis Qu\u00edstica<\/span>. Desde el Hospital Juan Cardona queremos darle divulgaci\u00f3n a esta enfermedad, que suele manifestarse en etapas muy tempranas de la vida.<\/p>\n<p><!--more--><\/p>\n<p>La fibrosis qu\u00edstica provoca la acumulaci\u00f3n de moco espeso y pegajoso en los pulmones, el tubo digestivo y otras \u00e1reas del cuerpo. Es uno de los tipos de enfermedad pulmonar cr\u00f3nica m\u00e1s com\u00fan en ni\u00f1os y adultos j\u00f3venes. Es una enfermedad potencialmente mortal.<\/p>\n<p><strong><span style=\"color: #ff255a;\">Causas<\/span><\/strong><br \/>\nLa fibrosis qu\u00edstica (FQ) es una enfermedad hereditaria, causada por un <span style=\"color: #ff255a;\">gen defectuoso<\/span> que lleva al cuerpo a producir un l\u00edquido anormalmente espeso y pegajoso llamado moco. Este moco se acumula en las <span style=\"color: #ff255a;\">v\u00edas respiratorias de los pulmones<\/span> y en el <span style=\"color: #ff255a;\">p\u00e1ncreas<\/span>.<br \/>\nEsta acumulaci\u00f3n de moco ocasiona infecciones pulmonares potencialmente mortales y serios problemas digestivos. Esta enfermedad tambi\u00e9n puede afectar las gl\u00e1ndulas sudor\u00edparas y el aparato reproductor masculino.<br \/>\nMillones de estadounidenses portan el gen de la fibrosis qu\u00edstica, pero no manifiestan ning\u00fan s\u00edntoma. Esto se debe a que una persona con esta enfermedad debe heredar dos genes defectuosos, uno de cada padre. La enfermedad es m\u00e1s frecuente entre aquellas personas descendientes de europeos del centro y norte.<br \/>\nA la mayor\u00eda de los ni\u00f1os con fibrosis qu\u00edstica se les diagnostica la enfermedad <span style=\"color: #ff255a;\">hacia los dos a\u00f1os de edad<\/span>. Para un peque\u00f1o n\u00famero, la enfermedad no se detecta hasta la edad de 18 a\u00f1os o m\u00e1s. Estos ni\u00f1os con frecuencia padecen una forma m\u00e1s leve de la enfermedad.<\/p>\n<p><strong><span style=\"color: #ff255a;\">S\u00edntomas<\/span><\/strong><br \/>\nLos s\u00edntomas en los <span style=\"color: #ff255a;\">reci\u00e9n nacidos<\/span> pueden abarcar:<br \/>\n1. Retraso en el crecimiento.<br \/>\n2. Incapacidad para aumentar de peso normalmente durante la ni\u00f1ez.<br \/>\n3. Ausencia de deposiciones durante las primeras 24 a 48 horas de vida.<br \/>\n4. Piel con sabor salado.Los s\u00edntomas relacionados con la <span style=\"color: #ff255a;\">funci\u00f3n intestinal<\/span> pueden abarcar:<br \/>\n1. Dolor abdominal a causa del estre\u00f1imiento grave.<br \/>\n2. Aumento de gases, meteorismo o un abdomen que parece hinchado (distendido).<br \/>\n3. N\u00e1useas e inapetencia.<br \/>\n4. Heces p\u00e1lidas o color arcilla, de olor f\u00e9tido, que tienen moco o que flotan.<br \/>\n5. P\u00e9rdida de peso.Los s\u00edntomas relacionados con los <span style=\"color: #ff255a;\">pulmones y los senos paranasales<\/span> pueden abarcar:<br \/>\n1. Tos o aumento de la mucosidad en los senos paranasales o los pulmones.<br \/>\n2. Fatiga.<br \/>\n3. Congesti\u00f3n nasal causada por los p\u00f3lipos nasales.<br \/>\n4. Episodios recurrentes de neumon\u00eda (los s\u00edntomas de neumon\u00eda en una persona con fibrosis qu\u00edstica abarcan fiebre, aumento de la tos y dificultad respiratoria, aumento de la mucosidad y p\u00e9rdida del apetito).<br \/>\n5. Dolor o presi\u00f3n sinusal causados por infecci\u00f3n o p\u00f3lipos. Los s\u00edntomas que se pueden notar <span style=\"color: #ff255a;\">posteriormente,\u00a0<span style=\"color: #000000;\">a lo largo de la vida<\/span><\/span>\u00a0son:<br \/>\n1. Esterilidad (en los hombres).<br \/>\n2. Inflamaci\u00f3n repetitiva del p\u00e1ncreas (pancreatitis).<br \/>\n3. S\u00edntomas respiratorios.<br \/>\n4. Dedos malformados.<br \/>\n<strong><span style=\"color: #ff255a;\">Pruebas y ex\u00e1menes<\/span><\/strong><br \/>\nExiste un <span style=\"color: #ff255a;\">examen de sangre<\/span> disponible para ayudar a detectar la fibrosis qu\u00edstica. El examen busca variaciones en un gen conocido como causante de la enfermedad. Sin embargo, existen muchos ex\u00e1menes capaces de detectarla, siendo aplicables unos u otros seg\u00fan el criterio facultativo.<br \/>\n<strong><span style=\"color: #ff255a;\">Tratamiento<\/span><\/strong><br \/>\nUn <span style=\"color: #ff255a;\">diagn\u00f3stico temprano<\/span> de FQ y un <span style=\"color: #ff255a;\">plan de tratamiento<\/span> pueden mejorar tanto la supervivencia como la calidad de vida. El control y vigilancia son muy importantes. Cuando sea posible, los pacientes deben recibir cuidados en cl\u00ednicas con especialidad en fibrosis qu\u00edstica. Cuando los ni\u00f1os llegan a la adultez, deben transferirse a un centro especializado en fibrosis qu\u00edstica para adultos.<\/p>\n<p><a href=\"http:\/\/www.fqgalicia.org\/\"><strong><span style=\"color: #ff255a;\">Grupos de apoyo<\/span><\/strong><\/a><br \/>\nUsted puede aliviar el estr\u00e9s causado por la enfermedad formando parte de un grupo de apoyo para la fibrosis qu\u00edstica. Compartir con otras personas que tengan experiencias y problemas en com\u00fan puede ayudar a que su familia no se sienta sola.<\/p>\n<p><strong><span style=\"color: #ff255a;\">Expectativas (pron\u00f3stico)<\/span><\/strong><br \/>\nLa mayor\u00eda de los ni\u00f1os con fibrosis qu\u00edstica permanecen con buena salud hasta que llegan a la adultez. Pueden participar en la mayor\u00eda de las actividades y asistir a la escuela. Muchos adultos j\u00f3venes con fibrosis qu\u00edstica terminan la universidad o encuentran empleo.<br \/>\nCon el tiempo, la enfermedad pulmonar empeora al punto en que la persona queda incapacitada. Actualmente, el per\u00edodo de vida promedio de las personas que padecen esta enfermedad y que viven hasta la adultez es de aproximadamente 37 a\u00f1os.<\/p>\n<p><strong><span style=\"color: #ff255a;\">Prevenci\u00f3n<\/span><\/strong><br \/>\nLa fibrosis qu\u00edstica no puede prevenirse. El hecho de realizar <span style=\"color: #ff255a;\">pruebas de detecci\u00f3n<\/span> en aquellas personas con antecedentes familiares de esta enfermedad puede detectar el gen de la fibrosis qu\u00edstica en muchos portadores.<\/p>\n<p>Consulte <a href=\"https:\/\/riberasalud.com\/juan-cardona\/el-hospital-juan-cardona-atiende-al-80-de-los-pacientes-de-hemodialisis-del-area-santiaria-de-ferrolterra\/\">aqu\u00ed<\/a> otros art\u00edculos sobre enfermedades cr\u00f3nicas. <!-- Start of HubSpot Analytics Code Not Loaded --><!-- End of HubSpot Analytics Code Not Loaded --><!-- Generated by the HubSpot Template Builder - template version 1.03 --><!-- end coded_template: id:5238321518 path:generated_layouts\/5238321516.html --><\/p>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n","protected":false,"gt_translate_keys":[{"key":"rendered","format":"html"}]},"excerpt":{"rendered":"<p>Ante la proximidad del D\u00eda Mundial de la Fibrosis Qu\u00edstica queremos dar divulgaci\u00f3n a esta enfermedad cr\u00f3nica.<\/p>\n","protected":false,"gt_translate_keys":[{"key":"rendered","format":"html"}]},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[4],"tags":[],"class_list":["post-3401","post","type-post","status-publish","format-standard","hentry","category-noticias-del-hospital-juan-cardona"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.6 - 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